Rare Liver and Biliary Tract Diseases

Surgical Management

Thilo Hackert, Aiste Gulla (Herausgeber)

Buch | Hardcover

III, 522 Seiten

2026
Springer International Publishing (Verlag)
978-3-032-15075-2 (ISBN)

Infos

Aim of this publication is to offer readers a comprehensive surgical textbook that addresses exclusively rare liver and biliary diseases in pediatric and adult populations. 

It will  explain the origin of these types of diseases and provide guidance about their clinical manifestation, diagnosis, and treatment options. State-of-the-art research in the areas will be presented.

Written by a multidisciplinary team of world-renowned experts, this textbook addresses the knowledge gap surrounding these rare diseases. Many medical professionals specialists as well as general practitioners are unfamiliar with these conditions due to their rarity. This book is designed for medical clinicians, including medical students and residents, PhD candidates, and postdoctoral researchers. Multiple specialties, such as oncology, surgery, pediatrics, and endocrinology, will find this book an invaluable reference.

 

Autor

Professor Thilo Hackert is the vice chairman of the Department of General, Visceral and Transplantation Surgery at the University Hospital in Heidelberg (Director Prof.M. W. Büchler). After receiving his medical degree from the University of Heidelberg, he continued surgical education in Heidelberg and specialized on visceral surgery with a focus on pancreatic diseases, both clinically and scientifically. He became head of the section for pancreatic surgery in 2014. A special focus has recently been laid on robotic pancreatic surgery which has been introduced in Heidelberg in 2016 and is increasingly performed for all types of pancreatic resections. He has worked in committees for National Guidelines (chronic pancreatitis, pancreatic cancer) as well as the European Guidelines for Cystic Tumors and is Council Member for Clinical Science in the European Pancreas Club.

 

Associate Professor Aiste Gulla is the Chief of the Solid Organ Transplantation Center at Vilnius Hospital Santaros Clinics. She received a medical degree from the University of Lithuanian Health Sciences, a master's degree from Johns Hopkins Carey Business School in the USA, and a Ph.D. in Medicine-Surgery from Vilnius University. She currently serves as the co-director of the Visceral Medicine and Transplantation Research Center at Vilnius University with the research focus on pancreas, liver and biliary system tumor single cell diagnostics, genetic drivers and microenvironment. Dr. Gulla recently implemented two surgical innovations in liver and pancreas patient care. Her center successfully adopted the use of a liver perfusion machine to improve liver transplantation outcomes and performed the first Pancreatic islet cell transplantation in the Baltics. Dr. Gulla is a recipient of K.Warren's HPB fellowship award established by IHPBA. She is also a member of multiple national and international liver and pancreas transplantation committees and serves on the board of the international experts for the "Guide to the quality and safety of organs for transplantation (9th edition)" established by the Council of Europe, European Directorate for the Quality of Medicines and HealthCare.

 

Inhalt

Chapter 1- Allagile's syndrome.- Chapter 2-Traumatic and post-surgical biliary tract diseases.- Chapter 3-Epithelioid hemangioendothelioma.- Chapter 4-Liver fluke.- Chapter 5-Mucinous cystic neoplasms.- Chapter 6- Embryologic rare liver tumors.- Chapter 7 Hepatobiliary Sarcoma.- Chapter 8-Caroli disease.- Chapter 9-Cryptogenic cirrhosis.- Chapter 10-Wilson's disease.- Chapter 11-Hemochromatosis.- Chapter 12- Biliary atresia.- Chapter 13-Alpha-1 antitrypsin deficiency.- Chapter 14-Cirrhosis secondary to prolonged total parental nutrition.- Chapter 15-Echinococcus.- Chapter 16-Fibrolamellar hepatocellular carcinoma (FL-HCC).- Chapter 17-Mesenchymal hamartoma.- Chapter 18-Intraductal papillary mucinous neoplasm of the biliary tract (IPMN-B).- Chapter 19-Extrahepatic biliary atresia.- Chapter 20-Hepatoblastoma.- Chapter 21-Congenital hepatic fibrosis.- Chapter 22-Budd Chiarri.- Chapter 23-Urea cycle deficiency.- Chapter 24-Mitochondrial disorders.- Chapter 25- Navajo neurohepatopathy.- Chapter 26-Familial intra-hepatic cholestasis (Byler disease).- Chapter 27-Obstructive biliary tract disease.- Chapter 28-Choledochal cysts.- Chapter 29-Pregnancy and liver diseases.- Chapter 30-Rare benign hepatic  cysts.- Chapter 31-Maple Syrup Urine diseases.- Chapter 32-Primary sclerosing cholangitis.- Chapter 33-Inflammatory pseudotumors.

Produkt-Details

• Erscheint lt. Verlag: 23.3.2026
• Zusatzinfo: III, 522 p. 75 illus., 48 illus. in color. With online files/update.
• Verlagsort: Cham
• Sprache: englisch
• Maße: 178 x 254 mm
• Themenwelt: Medizin / Pharmazie ► Medizinische Fachgebiete ► Chirurgie
• Schlagworte: intrahepatic cholestasis • Liver management • Metabolic liver • Rare liver tumors • Traumatic biliary tract
• ISBN-10: 3-032-15075-2 / 3032150752
• ISBN-13: 978-3-032-15075-2 / 9783032150752
• Zustand: Neuware